La enfermedad de Steinert es una rara miopatía hereditaria caracterizada por debilidad muscular generalizada, miotonía y afección multisistémica. Aunque los . A distrofia miotônica (DM), também conhecida como doença de Steinert1,2 é a forma mais comum no adulto, com prevalência estimada em 1 para PDF | La distrofia miotónica de Steinert (DM1) es una enfermedad hereditaria, caracterizada por desórdenes multisistémicos asociados a disfunción muscular.

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The myotony often worsens and obstetric complications increase; miscarriage, preterm delivery, hydrops fetalis, intrauterine death, difficulties in expulsion, intra and post partum haemorrhage. Progressive muscular dystrophy and myotonic disorders. Obstet Gynecol Surv, 41distrotia.

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Prenatal diagnosis of myotonic dystrophy by direct mutation analysis. Lancet, 2pp. To improve our services and products, we use steknert own or third parties authorized to show advertising related to client preferences through the analyses of navigation customer behavior.

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Myotonic dystrophy and heart disease: behavior of arrhythmic events and conduction disturbances

You can change the settings or obtain more information by clicking here. Eur J Pediatr,pp.

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